Is Anorectal Myectomy useful for Hirschsprung’s Disease and its Allied Disorders?

study of outcome and complications of anorectal myectomy in children with ultrashort segment hirschsprung’s disease

the term ultra short is not clearly defined in ultrashort-segment hirschsprung’s disease. the limited extent of the ultrashort-segment hirschsprung’s disease allows for treatment with extended sphincteromyectomy. in anal sphincter achalasia, anal sphincter dilatation under general anesthesia may be sufficient to treat the condition; in cases with persistent constipation, sphincteromyectomy is i...

Hirschsprungs disease with congenital hypothyroidism.

We report a female newborn baby who presented with vomiting and abdominal distension on day 21 of life. Examination revealed facial puffiness, open posterior fontanelles, dry skin, cold peripheries and prominent abdominal veins with visible peristalsis. Barium enema revealed dilated proximal colon, empty rectum, funnel like transition zone between proximal dilated and distal constricted bowel. ...

Is sentinel node mapping useful in anorectal melanoma?

Anorectal melanoma (AM) is a rare disease and few guidelines have been established regarding its therapeutic management. Wide local excision, or less frequently, abdominoperineal resection is the treatment of choice. We present a female patient with an excised AM who was submitted to our Nuclear Medicine department for sentinel lymph node (SLN) mapping of the area. Under rigid proctoscopy the a...

Anorectal myectomy in treatment of ultrashort segment Hirschsprung's disease. Report of 26 cases.

A diagnosis of Hirschsprung's disease should be considered in children with constipation. An accurate neonatal history of bowel function and testing of anorectal pressure responses will aid the diagnosis. In the period 1971-75 inclusive, 140 children, aged 6 months to 14 years, were investigated by anorectal manometry. 26 showed a failed inhibition response to rectal dilatation, suggesting Hirs...

Leukæmia and Allied Disorders